A Brief Study about Dyke Davidoff Masson Syndrome: Rare Cause of Cerebral Hemiatrophy

Dyke-Davidoff-Masson syndrome (DDMS) is an uncommon condition, characterized radiologically by cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses, of unknown frequency resulting from brain injury due to large no of causes; especially in early life. Mostly presents early in life with seizures, learning difficulty, contralateral hemiparesis and facial symmetry. Here we present a case of 11 months old female child with developmental delay, visual abnormality, microcephaly and spastic hemiplegia. CT-brain done which was suggestive of infantile type of cerebral hemiatrophy or DDMS. DDMS is caused by an insult to growing brain either cerebrum in utero when maturation of calvarium has not been completed, or during early life due to damage to brain.